Results The rate of the inner ear malformation in congenital sensorineural deafness in the tested children reaches to 46.8%.

• 结果在所测试的先天性感音神经性耳聋患儿中内耳畸形的比率达到了46.；8%25，发病率很高，且听力测试多为重度或极重度感音神经性耳聋。