Primary adenocarcinoma of the middle ear is very rare and its origin is still controversial.Before making a confirmative diagnosis, metastatic tumor should be ruled out.

• 摘要中耳原发性腺癌是一种起源自中耳腺体极为罕见之疾病，一般对于是否起源于制造耳垢或是耳蜡的腺体所产生的外耳道恶性肿瘤局部转移而来仍多有争议。