Methods:The clinical traits were studied in 41 PKMD patients,and routine EEG was recorded in all of them. Twenty one of the 41 patients underwent ambulant EEG recording and limb movement evoked activation was done in 8 patients during EEG monitoring.

• 方法 :详细观察PKMD4 1例的临床特征 ,全部进行了常规脑电记录 ,2 1例进行Holter脑电长时间监测 ,在脑电图监测下 8例作运动诱发试验。