Major clinical presentations are hypertension with or without encephalopathy, ischemia of brain, kidney, retina, and extremities, and vascular bruit.

• 此病临床表现多样性，主要以高血压、大脑、肾脏、视网膜及四肢之缺血性病变较常见。六例已进入慢性期，一例在急性期被诊断。