In conclusion, especially patients with a hepaticojejunostomy, those with an early diagnosis of NAS, and those with NAS presenting at the level of the peripheral branches of the biliary tree, are at risk for progressive disease with severe outcome.

• 结论：肝移植术中行肝十二指肠吻合，早期诊断为NAS以及狭窄部位处于胆道系统的周围支是疾病进展的危险因素。